Plays an important role in the degradation of dermatan and keratan sulfates.Oshima A., Proc. Natl. Acad. Sci. U.S.A. 84:685-689(1987).Totoki Y., Submitted (APR-2005) to the EMBL/GenBank/DDBJ databases. Hillier L.W., Nature 424:157-164(2003).
Host
Rabbit
Immunogen
Synthesized peptide derived from internal of Human GUSB.
Involvement In Disease
Mucopolysaccharidosis 7 (MPS7)
Raised In
Rabbit
Reactivity
Human
Regulatory
RUO
Relevance
Plays an important role in the degradation of dermatan and keratan sulfates.
Oshima A., Proc. Natl. Acad. Sci. U.S.A. 84:685-689(1987). Totoki Y., Submitted (APR-2005) to the EMBL/GenBank/DDBJ databases. Hillier L.W., Nature 424:157-164(2003).
Species
Homo Sapiens (Human)
Specificity
The antibody detects endogenous levels of total GUSB protein.